Suchergebnisse

Introduction: A crucible of race : historicizing the sexual economy of Cuban social identities -- Ascendant capitalism and white intellectual re-assessments of Afro-Cuban social value to 1820 -- Slavery and Afro-Cuban family formation during Cuba's economic awakening, 1763-1820 -- The illegal slave trade and the Cuban sexual economy of race, 1820-1867 -- Nineteenth-century racial myths and the familial corruption of whiteness -- Afro-Cuban family emancipation, 1868-1886 -- "Regenerating" the Afro-Cuban family, 1886-1940 -- Mestizaje literary visions and Afro-Cuban genealogical memory, 1920-1958 -- Epilogue: Revolutionary social morality and the multi-racial national family, 1959-2000

This essay reviews the following works:Freedom from Liberation: Slavery, Sentiment, and Literature in Cuba. By Gerard Aching. Bloomington: Indiana University Press, 2015. Pp. ix + 241. $48.00 hardcover. ISBN: 9780253016935.Slavery and Politics: Brazil and Cuba, 1790–1850. By Rafael Marquese, Tâmis Peixoto Parron, and Márcia Regina Berbel. Translated by Leonardo Marques. Albuquerque: University of New Mexico Press, 2016. Pp. 1 + 351. $29.95 paperback. ISBN: 9780826356482.Divining Slavery and Freedom: The Story of Domingos Sodré, an African Priest in Nineteenth-Century Brazil. By João José Reis. Translated by H. Sabrina Gledhill. New York: Cambridge University Press, 2015. Pp. xi + 351. $32.99 paperback. ISBN: 9781107439092.Ever Faithful: Race, Loyalty, and the Ends of Empire in Spanish Cuba. By David Sartorius. Durham, NC: Duke University Press, 2014. Pp. vi + 312. $24.95 paperback. ISBN: 9780822355939.The Politics of the Second Slavery. Edited by Dale W. Tomich. Fernand Braudel Center Studies in Historical Social Science. Ithaca: State University New York Press, 2016. Pp. xii + 280. $25.95 paperback. ISBN: 9781438462363.

Abstract
With the social reproduction of slavery in colonial Cuba as its center point, this essay draws on the recent historiographical acknowledgment of the way vassalage mediated the often starkly drawn social distinctions between whites and enslaved people within colonial Spanish America. Inside the region's emergent, capitalist political economy, feudal vassalage continued to define each social sector's rights and responsibilities vis-á-vis the Spanish Crown. The rights of enslaved vassals derived from their potential contributions to the Spanish monarchy's imperial survival, in their capacity to populate the extensive empire with loyal Catholic subjects and potential military defenders. These concerns also justified the Spanish monarchial state's ability to intervene between its slaveholding vassals and its enslaved vassals, by limiting private property rights over enslaved people and operating in ways that did not fully conform to capitalist profit motives. Awareness of such sovereign-vassal interdependencies challenges historians to broaden their understanding of the relationship between capitalism and slavery to include the remnants of feudal social-political forms, even into the nineteenth century.

Este ensayo es una historia de ideas, un examen de como los intelectuales afrocubanos "se imaginaron" la nacion cubana y el papel de la gente de color dentro de la misma. El trabajo se centra en la manera en que los cambios en los conceptos de "civilizacion" y "ciudadania" impactaron sobre al vida politica y social afrocubana. Durante la primera etapa constitucional en Cuba (1902-1940), la nocion de civilizacion fue manipulada por los intelectuales afrocubanos de clase media en sus esfuerzos por ampliar ideas afrocubanas sobre ciudadania hacia una orientacion mas abarcadora racialmente que sugeria una armoniosa fusion de elementos basados en las culturas europeas y africanas. (Cuba Stud/DÜI)

"Written and evaluated by experienced teachers and teacher educators, this third edition of the popular series brings an entirely fresh approach, updating the design and illustrations and matching the content perfectly to the latest curriculum documentation.What's new?* A thorough review from the ground up, ensuring full curriculum coverage and a contemporary, up-to-date approach* 'Word power' feature introduces new vocabulary and concepts* 'Think about it' feature makes cross-curricular links and encourages critical-thinking and problem-solving* Teaching information clearly explained, and followed by step-by-step, graded activities".

"Written and evaluated by experienced teachers and teacher educators, this third edition of the popular series brings an entirely fresh approach, updating the design and illustrations and matching the content perfectly to the latest curriculum documentation.What's new?* A thorough review from the ground up, ensuring full curriculum coverage and a contemporary, up-to-date approach* 'Word power' feature introduces new vocabulary and concepts* 'Think about it' feature makes cross-curricular links and encourages critical-thinking and problem-solving* Teaching information clearly explained, and followed by step-by-step, graded activities".

"Written and evaluated by experienced teachers and teacher educators, this third edition of the popular series brings an entirely fresh approach, updating the design and illustrations and matching the content perfectly to the latest curriculum documentation.What's new?* A thorough review from the ground up, ensuring full curriculum coverage and a contemporary, up-to-date approach* 'Word power' feature introduces new vocabulary and concepts* 'Think about it' feature makes cross-curricular links and encourages critical-thinking and problem-solving* Teaching information clearly explained, and followed by step-by-step, graded activities".

Brothers at Bat describes the Acerra family and their love for baseball, providing students with insights into 1930's family culture and community life. Students examine the characteristics of the Acerras that enabled them to develop and demonstrate their team spirit. Creating a Power Point slide show displaying their own diverse characteristics and team spirit from a classroom perspective will engage students' creativity and knowledge. A trading card created by each student uniquely representing the student and will be used in a Trading Card Collection displaying the different cultures and interests that come together to make one classroom community team.

Importance: Juvenile amyotrophic lateral sclerosis (ALS) is a rare form of ALS characterized by age of symptom onset less than 25 years and a variable presentation. Objective: To identify the genetic variants associated with juvenile ALS. Design, Setting, and Participants: In this multicenter family-based genetic study, trio whole-exome sequencing was performed to identify the disease-associated gene in a case series of unrelated patients diagnosed with juvenile ALS and severe growth retardation. The patients and their family members were enrolled at academic hospitals and a government research facility between March 1, 2016, and March 13, 2020, and were observed until October 1, 2020. Whole-exome sequencing was also performed in a series of patients with juvenile ALS. A total of 66 patients with juvenile ALS and 6258 adult patients with ALS participated in the study. Patients were selected for the study based on their diagnosis, and all eligible participants were enrolled in the study. None of the participants had a family history of neurological disorders, suggesting de novo variants as the underlying genetic mechanism. Main Outcomes and Measures: De novo variants present only in the index case and not in unaffected family members. Results: Trio whole-exome sequencing was performed in 3 patients diagnosed with juvenile ALS and their parents. An additional 63 patients with juvenile ALS and 6258 adult patients with ALS were subsequently screened for variants in the SPTLC1 gene. De novo variants in SPTLC1 (p.Ala20Ser in 2 patients and p.Ser331Tyr in 1 patient) were identified in 3 unrelated patients diagnosed with juvenile ALS and failure to thrive. A fourth variant (p.Leu39del) was identified in a patient with juvenile ALS where parental DNA was unavailable. Variants in this gene have been previously shown to be associated with autosomal-dominant hereditary sensory autonomic neuropathy, type 1A, by disrupting an essential enzyme complex in the sphingolipid synthesis pathway. Conclusions and Relevance: These data broaden the phenotype associated with SPTLC1 and suggest that patients presenting with juvenile ALS should be screened for variants in this gene.

International audience ; Importance: Juvenile amyotrophic lateral sclerosis (ALS) is a rare form of ALS characterized by age of symptom onset less than 25 years and a variable presentation.Objective: To identify the genetic variants associated with juvenile ALS.Design, setting, and participants: In this multicenter family-based genetic study, trio whole-exome sequencing was performed to identify the disease-associated gene in a case series of unrelated patients diagnosed with juvenile ALS and severe growth retardation. The patients and their family members were enrolled at academic hospitals and a government research facility between March 1, 2016, and March 13, 2020, and were observed until October 1, 2020. Whole-exome sequencing was also performed in a series of patients with juvenile ALS. A total of 66 patients with juvenile ALS and 6258 adult patients with ALS participated in the study. Patients were selected for the study based on their diagnosis, and all eligible participants were enrolled in the study. None of the participants had a family history of neurological disorders, suggesting de novo variants as the underlying genetic mechanism.Main outcomes and measures: De novo variants present only in the index case and not in unaffected family members.Results: Trio whole-exome sequencing was performed in 3 patients diagnosed with juvenile ALS and their parents. An additional 63 patients with juvenile ALS and 6258 adult patients with ALS were subsequently screened for variants in the SPTLC1 gene. De novo variants in SPTLC1 (p.Ala20Ser in 2 patients and p.Ser331Tyr in 1 patient) were identified in 3 unrelated patients diagnosed with juvenile ALS and failure to thrive. A fourth variant (p.Leu39del) was identified in a patient with juvenile ALS where parental DNA was unavailable. Variants in this gene have been previously shown to be associated with autosomal-dominant hereditary sensory autonomic neuropathy, type 1A, by disrupting an essential enzyme complex in the sphingolipid synthesis pathway.Conclusions and ...

International audience ; Importance: Juvenile amyotrophic lateral sclerosis (ALS) is a rare form of ALS characterized by age of symptom onset less than 25 years and a variable presentation.Objective: To identify the genetic variants associated with juvenile ALS.Design, setting, and participants: In this multicenter family-based genetic study, trio whole-exome sequencing was performed to identify the disease-associated gene in a case series of unrelated patients diagnosed with juvenile ALS and severe growth retardation. The patients and their family members were enrolled at academic hospitals and a government research facility between March 1, 2016, and March 13, 2020, and were observed until October 1, 2020. Whole-exome sequencing was also performed in a series of patients with juvenile ALS. A total of 66 patients with juvenile ALS and 6258 adult patients with ALS participated in the study. Patients were selected for the study based on their diagnosis, and all eligible participants were enrolled in the study. None of the participants had a family history of neurological disorders, suggesting de novo variants as the underlying genetic mechanism.Main outcomes and measures: De novo variants present only in the index case and not in unaffected family members.Results: Trio whole-exome sequencing was performed in 3 patients diagnosed with juvenile ALS and their parents. An additional 63 patients with juvenile ALS and 6258 adult patients with ALS were subsequently screened for variants in the SPTLC1 gene. De novo variants in SPTLC1 (p.Ala20Ser in 2 patients and p.Ser331Tyr in 1 patient) were identified in 3 unrelated patients diagnosed with juvenile ALS and failure to thrive. A fourth variant (p.Leu39del) was identified in a patient with juvenile ALS where parental DNA was unavailable. Variants in this gene have been previously shown to be associated with autosomal-dominant hereditary sensory autonomic neuropathy, type 1A, by disrupting an essential enzyme complex in the sphingolipid synthesis pathway.Conclusions and ...

International audience ; Importance: Juvenile amyotrophic lateral sclerosis (ALS) is a rare form of ALS characterized by age of symptom onset less than 25 years and a variable presentation.Objective: To identify the genetic variants associated with juvenile ALS.Design, setting, and participants: In this multicenter family-based genetic study, trio whole-exome sequencing was performed to identify the disease-associated gene in a case series of unrelated patients diagnosed with juvenile ALS and severe growth retardation. The patients and their family members were enrolled at academic hospitals and a government research facility between March 1, 2016, and March 13, 2020, and were observed until October 1, 2020. Whole-exome sequencing was also performed in a series of patients with juvenile ALS. A total of 66 patients with juvenile ALS and 6258 adult patients with ALS participated in the study. Patients were selected for the study based on their diagnosis, and all eligible participants were enrolled in the study. None of the participants had a family history of neurological disorders, suggesting de novo variants as the underlying genetic mechanism.Main outcomes and measures: De novo variants present only in the index case and not in unaffected family members.Results: Trio whole-exome sequencing was performed in 3 patients diagnosed with juvenile ALS and their parents. An additional 63 patients with juvenile ALS and 6258 adult patients with ALS were subsequently screened for variants in the SPTLC1 gene. De novo variants in SPTLC1 (p.Ala20Ser in 2 patients and p.Ser331Tyr in 1 patient) were identified in 3 unrelated patients diagnosed with juvenile ALS and failure to thrive. A fourth variant (p.Leu39del) was identified in a patient with juvenile ALS where parental DNA was unavailable. Variants in this gene have been previously shown to be associated with autosomal-dominant hereditary sensory autonomic neuropathy, type 1A, by disrupting an essential enzyme complex in the sphingolipid synthesis pathway.Conclusions and ...